An uncommon cause of multiple pulmonary nodules; hereditary hemorrhagic telangiectasia
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Tarih
2016
Dergi Başlığı
Dergi ISSN
Cilt Başlığı
Yayıncı
Turkish Assoc Tuberculosis & Thorax
Erişim Hakkı
info:eu-repo/semantics/openAccess
Özet
Hereditary hemorrhagic telangiectasia ( HHT), or Rendu-Osler-Weber syndrome ( ROWS) is a very rare hereditary disease. The diagnosis is based on the clinical findings such as recurrent epistaxis, telangiectases, visceral arteriovenous malformations (AVMs) and family history. AVMs are found in the liver, lung or brain and could mimick the masses of these organs. Radiologic evaluation plays a critical role during diagnostic and therapeutic management of ROWS. Hence, radiologists should be aware of the diagnosis of HHT in the patients with AVMs, history of epistaxis and family history. We report a patient with multiple pulmonary AVMs secondary to HHT who has referred to our interventional radiology department for computed tomography guided transthorasic lung biopsy procedure with suspicious of malignancy.
Açıklama
Anahtar Kelimeler
Hereditary hemorrhagic telangiectasia, pulmonary arteriovenous malformations, computed tomography
Kaynak
Tuberkuloz Ve Torak-Tuberculosis and Thorax
WoS Q Değeri
N/A
Scopus Q Değeri
Q3
Cilt
64
Sayı
1